People with PKU cannot break down foods containing protein in the usual way, due to the lack of an enzyme the body cannot properly deal with the amino acid phenylalanine. When PKU is detected early and treated with a special diet, children are able to reach their full potential. A key element in the management of PKU is the use of PKU formula, which provides all the amino acids found in protein but with little or no phenylalanine. PKU formulas support adequate intake of protein in combination with the small allowance of regular dietary protein.
